https://doi.org/10.4081/reumatismo.2014.753

Perivascular fibrosis and IgG4-related disease: a case report

Vol. 66 No. 3 (2014)
Submitted: 23 May 2014
Accepted: 30 August 2014
Published: 6 November 2014
Immunoglobulin G4-related disease, Perivascular fibrosis, Retroperitoneal fibrosis, Aortic aneurysm.
Abstract Views: 1849
PDF: 1009
Publisher's note
All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.

Authors

S. Monti
saram86@libero.it
U.O. Reumatologia, Università di Pavia, IRCCS Fondazione Policlinico S. Matteo, Pavia, Italy.
G. Crepaldi
U.O. Reumatologia, Università di Pavia, IRCCS Fondazione Policlinico S. Matteo, Pavia, Italy.
A. Peri
U.O. Chirurgia Generale, Università di Pavia, IRCCS Fondazione Policlinico S. Matteo, Pavia, Italy.
A. Pietrabissa
U.O. Chirurgia Generale, Università di Pavia, IRCCS Fondazione Policlinico S. Matteo, Pavia, Italy.
P. Morbini
U.O. Anatomia Patologica, Università di Pavia, IRCCS Fondazione Policlinico S. Matteo, Pavia, Italy.
F. Bobbio-Pallavicini
U.O. Reumatologia, Università di Pavia, IRCCS Fondazione Policlinico S. Matteo, Pavia, Italy.
C. Montecucco
U.O. Reumatologia, Università di Pavia, IRCCS Fondazione Policlinico S. Matteo, Pavia, Italy.
R. Caporali
U.O. Reumatologia, Università di Pavia, IRCCS Fondazione Policlinico S. Matteo, Pavia, Italy.
Immunoglobulin G4-related disease (IgG4-RD) is a newly recognized fibroinflammatory condition which can potentially involve any organ. Some characteristic histopathologic features with lymphoplasmacytic infiltrate, an increased number of IgG4+ cells, storiform fibrosis and obliterative phlebitis are the mainstay for diagnosis. Serum IgG4 levels often increase. We report the case of a patient with perivascular fibrotic lesions involving the aortic arch and the splenic hilum, with a surgical biopsy-proven diagnosis of IgG4-related disease. The patient is now undergoing a low-dose corticosteroid maintenance therapy without evidence of new localizations of the disease. This case highlights the need for increasing awareness and recognition of this new, emerging clinical condition.

Dimensions

Altmetric

PlumX Metrics

Downloads

Download data is not yet available.

Citations

Crossref
Scopus
Google Scholar
Europe PMC

Supporting Agencies

none

How to Cite

Monti, S., Crepaldi, G., Peri, A., Pietrabissa, A., Morbini, P., Bobbio-Pallavicini, F., … Caporali, R. (2014). Perivascular fibrosis and IgG4-related disease: a case report. Reumatismo, 66(3), 245–248. https://doi.org/10.4081/reumatismo.2014.753

Authors who publish with this journal agree to the following terms:

  1. Authors retain copyright and grant the journal right of first publication with the work simultaneously licensed under a Creative Commons Attribution License that allows others to share the work with an acknowledgement of the work's authorship and initial publication in this journal.
  2. Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
  3. Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work.

Similar Articles

<< < 4 5 6 7 8 9 10 11 12 13 > >> 

You may also start an advanced similarity search for this article.