https://doi.org/10.4081/reumatismo.2011.97

Primary Sjögren syndrome: report of a 10 years old girl with local edema and positivity of anti SS-A and anti SS-B autoantibodies

Vol. 63 No. 2 (2011)
Sjögren syndrome, anti Sjögren antigen, anti SS-A, anti SS-B.
Abstract Views: 1267
PDF: 816
Publisher's note
All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.

Authors

E. Shahi
editshahi@hotmail.com
U.O. di Reumatologia dell’età evolutiva, Dipartimento di Reumatologia, Università degli Studi di Milano, Istituto G. Pini, Italy.
C. Donati
U.O. di Reumatologia dell’età evolutiva, Dipartimento di Reumatologia, Università degli Studi di Milano, Istituto G. Pini, Italy.
M. Gattinara
U.O. di Reumatologia dell’età evolutiva, Dipartimento di Reumatologia, Università degli Studi di Milano, Istituto G. Pini, Italy.
I. Pontikaki
U.O. di Reumatologia dell’età evolutiva, Dipartimento di Reumatologia, Università degli Studi di Milano, Istituto G. Pini, Italy.
V. Gerloni
U.O. di Reumatologia dell’età evolutiva, Dipartimento di Reumatologia, Università degli Studi di Milano, Istituto G. Pini, Italy.
Sjögren-Larsson syndrome (SLS) is an autoimmune disease, uncommon in childhood. We report a case of SLS in a 10-year-old girl with a history of tumor, calor and rubor in the back of her toes almost every month, which resolved in 4-5 days without therapy. She did not complain of dry mouth or dry eyes. The laboratory fi ndings showed high infl ammation markers, rheumatoid factor 128 IU, Waaler-Rose 256 IU, anti nuclear antibody (ANA) 1/640, SSA (anti Sjögren antigen A) and SSB (anti Sjögren antigen B) positive and hypergammaglobulinemia. The Schirmer’s test resulted to be pathologic, the ultrasonography images and biopsy of minor salivary glands revealed focal periductal lymphocytic infi ltrate and sialoduct ectasia class IV of juvenile Sjögren syndrome. The juvenile Sjögren syndrome is frequently under-diagnosed. Clinical manifestations in children might be different from the adult form, although laboratory fi ndings may be similar to those found in adults.

Dimensions

Altmetric

PlumX Metrics

Downloads

Download data is not yet available.

Citations

Crossref
Scopus
Google Scholar
Europe PMC

How to Cite

Shahi, E., Donati, C., Gattinara, M., Pontikaki, I., & Gerloni, V. (2011). Primary Sjögren syndrome: report of a 10 years old girl with local edema and positivity of anti SS-A and anti SS-B autoantibodies. Reumatismo, 63(2), 97–100. https://doi.org/10.4081/reumatismo.2011.97

Authors who publish with this journal agree to the following terms:

  1. Authors retain copyright and grant the journal right of first publication with the work simultaneously licensed under a Creative Commons Attribution License that allows others to share the work with an acknowledgement of the work's authorship and initial publication in this journal.
  2. Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgement of its initial publication in this journal.
  3. Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work.

Similar Articles

<< < 14 15 16 17 18 19 20 21 22 23 > >> 

You may also start an advanced similarity search for this article.