https://doi.org/10.4081/reumatismo.2024.1669
Wunderlich syndrome as a rare complication of polyarteritis nodosa: a case report
Submitted: 23 October 2023
Accepted: 2 January 2024
Published: 22 March 2024
Accepted: 2 January 2024
Abstract Views: 438
PDF: 293
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All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.
Authors
Spontaneous subcapsular and perirenal hemorrhage, known as Wunderlich syndrome (WS), is a rare clinical manifestation of polyarteritis nodosa (PAN). We report a case of a 48-year-old male with a history of recurrent episodes of leg muscle tenderness and dysesthesia, bilateral flank pain, painful nodular skin lesions in the lower limbs, weight loss, and difficult-to-control arterial hypertension. The abdominopelvic computed tomography angiography showed a large left perirenal hematoma, leading to the patient’s admission to the intensive care unit. After the exclusion of infectious or neoplastic foci, the patient was diagnosed with PAN and started intravenous methylprednisolone pulses with a good response. Since WS is a rare initial clinical manifestation of PAN, an early diagnosis and aggressive treatment will significantly improve clinical outcomes.
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How to Cite
Oliveira, D., Martins, A., Martins, F., Rato, M., Pinheiro, F., Fonseca, D., … Costa, L. (2024). Wunderlich syndrome as a rare complication of polyarteritis nodosa: a case report. Reumatismo, 76(1). https://doi.org/10.4081/reumatismo.2024.1669
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