https://doi.org/10.4081/reumatismo.2024.1641
Adult ocular adnexal xanthogranulomatous disease associated with immunoglobulin G4-related disease: an unusual association
Submitted: 29 August 2023
Accepted: 5 December 2023
Published: 22 March 2024
Accepted: 5 December 2023
Abstract Views: 976
PDF: 201
Publisher's note
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All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.
Authors
Adult-onset xanthogranuloma (AOX) and immunoglobulin G4-related disease (IgG4-RD) are uncommon fibrosing conditions that may exhibit localized ocular manifestations and occasionally systemic symptoms. These conditions exhibit overlapping clinical and histological features, suggesting a potential correlation between them, although their exact relationship remains unclear. This paper presents the case of a black male patient exhibiting typical histological indications of both AOX and IgG4-RD. The patient responded positively to corticosteroid treatment.
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How to Cite
de Santana, A., Castro de Oliveira Figueirôa, M., Souza Pedreira, A., Behrens Pinto, G., & Santiago, M. (2024). Adult ocular adnexal xanthogranulomatous disease associated with immunoglobulin G4-related disease: an unusual association. Reumatismo, 76(1). https://doi.org/10.4081/reumatismo.2024.1641
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