@article{Monti_Crepaldi_Peri_Pietrabissa_Morbini_Bobbio-Pallavicini_Montecucco_Caporali_2014, title={Perivascular fibrosis and IgG4-related disease: a case report}, volume={66}, url={https://www.reumatismo.org/reuma/article/view/reumatismo.2014.753}, DOI={10.4081/reumatismo.2014.753}, abstractNote={Immunoglobulin G4-related disease (IgG4-RD) is a newly recognized fibroinflammatory condition which can potentially involve any organ. Some characteristic histopathologic features with lymphoplasmacytic infiltrate, an increased number of IgG4+ cells, storiform fibrosis and obliterative phlebitis are the mainstay for diagnosis. Serum IgG4 levels often increase. We report the case of a patient with perivascular fibrotic lesions involving the aortic arch and the splenic hilum, with a surgical biopsy-proven diagnosis of IgG4-related disease. The patient is now undergoing a low-dose corticosteroid maintenance therapy without evidence of new localizations of the disease. This case highlights the need for increasing awareness and recognition of this new, emerging clinical condition.}, number={3}, journal={Reumatismo}, author={Monti, S. and Crepaldi, G. and Peri, A. and Pietrabissa, A. and Morbini, P. and Bobbio-Pallavicini, F. and Montecucco, C. and Caporali, R.}, year={2014}, month={Nov.}, pages={245–248} }